A rare round cell tumour

A Young girl of 20 years presented with anaphylaxis to blue berries. Patient had two similar episodes which resolved with adrenaline. But patient developed progressive cough and dyspnoea over the next few weeks. Chest Xray was suggestive of anterior mediastinal mass. CECT of thorax revealed a malignancy . The Histopathology was suggestive of a round cell tumour (sheets of small round cells with scanty cytoplasm ) . Desmoplastic tumour was diagnosed on immunohistochemistry. Patient was referred for radiotherapy and chemotherapy as CT scan showed involvement of SVC and esophageal encashment.

Patient denied further treatment as she wanted to get a second opinion.

Desmoplastic tumours are usually found in abdomen and is usually seen among the males . Other differential diagnoses for anterior mediastinal tumours are

Lymphoma , Thymoma

Unknown's avatar

Author: Oncoknowledge

I am a General Internal Medicine doctor with special interest in Oncology previously worked in India and currently working with NHS. I am actively interested in cancer Prevention, screenings and treatment modalities. I actively encourage most modern modalities of treatments in Cancer and have been involved in various Cancer MDTs . I am also involved in various academic programs of Cancer and Infections.

Leave a comment